Encephalo 🧠
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πŸ”° USMLE materialiga asoslangan
πŸ”° MRT/KT
πŸ”° Terapiya
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πŸ“Œ Bel spinalnaya blokadasi

Ko'pchilikda beldagi og'riq blokadadan keyin qolib ketadi.


@firstaidstep1
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πŸ“Œ Bachadon MRT

Bachadonda, hali endigina maktabni bitirgan qizda kattakon mioma...

Farzandlaringizni tekshirtirib turing.


@firstaidstep1
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πŸ“Œ Hyperammonemia

#biochemistry

πŸ”°Mechanism

πŸ”˜ Flapping tremor(asterixis)
πŸ”˜ Vomiting
πŸ”˜ Cerebral edema
πŸ”˜ Slurring of speech
πŸ”˜ Blurring of vision
πŸ”˜ TCA cycle inhibition

πŸ›‘YouTube πŸ‘‡
https://www.youtube.com/embed/L0pi1sW6WfM

@firstaidstep1
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πŸ“ŒPhenylketonuria

πŸ›‘ YouTube πŸ‘‡
https://youtu.be/qObJYKSTnHM?si=i-NyY0eBKYMwZKZK

πŸ“Œ Varying degrees of clinical severity :
πŸ”˜Fetal growth restrictions
πŸ”˜ Microcepahaly
πŸ”˜ Intellectual disability
πŸ”˜ Congenital hart defects
πŸ”˜ Seizures
πŸ”˜ Hipopigmented skin
πŸ”˜ Eczema
πŸ”˜ Musty body odor

βœ… Ko'ramiz va share qilamiz
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πŸ“ŒBemorning boshi MRT qilindi, unda SFENOIDIT aniqlandi.

Ko'pincha burun-tomoq kasalliklaridan keyin kuzatiladigan burun atrofidagi bo'shliqlar yallig’lanadi. Gaymorit, frontit va mana bu bemorga o'xshab sfenoiditga sabab bo'ladi.

Gaymorit bo'lganlardan so'ranglar og'riq qanday bo'lishini aytadi, a buni og'rig'i bundan battar...

@firstaidstep1
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πŸ“Œ Maple syrup urine disease | Alkaptonuria

πŸ”˜ Vomiting
πŸ”˜ Poor feeding
πŸ”˜ Burnt sugar
πŸ”˜ Neurology signs
πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…πŸ”…
πŸ”˜ Bluish-black connective tissue
πŸ”˜ Bluish black ear cartilage
πŸ”˜ Ochronosis
πŸ”˜ Arthralgia

Ko'ramiz va share qilamiz ➑️

πŸ›‘YouTube πŸ‘‡
https://youtube.com/watch?v=53MZhu0zm7M&si=hkVTlvXnUSP8FvZ9
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πŸ“ŒSon suyagi boshchasi artrozi yoki son suyak boshchasi osteoartridi ham deb ataladi.

πŸ”˜ Bog'im sohasida og'riq, bu oyoqning pastki sohasiga ham berishi mumkin.
πŸ”˜ Qattiqlik
πŸ”˜ Cheklangan harakat(yurishda, yugirishda, egilishda, kundalik ishlarni bajarishda qiyinchilik)

❗️Erta aniqlash uchun MRT tekshiruvi zarur.

@firstaidstep1
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πŸ“Œ HOMOCYSTINURIA

πŸ”ΊHOMOCYstinuria
πŸ”˜ Homocystinuria
πŸ”˜ Osteoporosis
πŸ”˜ Marfanoid habitus
πŸ”˜ Ocular changes
πŸ”˜ Cardiovascular effects
πŸ”˜ kYphosis

πŸ”»Other effects:
πŸ”˜ Intellectual disability
πŸ”˜ Hipopigmented skin

πŸ›‘YouTube πŸ‘‡
https://www.youtube.com/embed/1GDWb5kP-o8
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πŸ“Œ Bo'yin sohasi MRT.

Bemorda "ΠΌΠΎΡ‰Π½Ρ‹ΠΉ" disk grijasi bor.

Bo'yindagi grija, beldagi grijadan ko'ra xavfli. Sababi bo'yin umurtqalaridan orqa miya o'tgan. Operatsiyasi ham bir muncha qiyin.

@firstaidstep1
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πŸ“ŒBel sohasi MRT

2003-yil qiz belida 6.0 mm grija. Yana bechorada belida qiyshayish ham bor.

Ko'p o'tirib ishlar ekan, og'ir yuk ko'tarmagan. Grija faqat og'ir yukdan keyin chiqib qolmaydi.

Lecheniya qilgandan keyin ham asrab-avaylamasa o'zini foydasi bo'lmay qoladi. ❗️❗️❗️❗️


@firstaidstep1
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πŸ“Œ Cystinuria and Organic acidemias

πŸ”˜ Cystine stones(hexagonal)
πŸ”˜ Propionic acidemia
πŸ”˜ Methilmalonic acidemia
πŸ”˜ Other clinical symptoms




πŸ›‘YouTube πŸ‘‡
https://youtu.be/yOxFQ1TDmmQ?si=d74HYUyWPx5WnK2d


@firstaidstep1
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πŸ“Œ Apocrinitis yoki Hidradenitis axillaris( Qo'ltiq osti ter bezlarining yallig’lanishi)

Gidradenitga ko'pincha kasallandiπŸ‘‡

πŸ”˜ Semiz odamlar(asosan ayollar)
πŸ”˜ Chekuvchilar
πŸ”˜ Acnega moyillar

Kasallikni viruslar ham keltirib chiqaradiyu, lekin asosan bakterilayarπŸ‘‡
πŸ”° S. aureus
πŸ”° streptococcuslar
πŸ”° Escherichia coli
πŸ”° Proteus mirabilis
πŸ”° Pseudomanas aeruginosa


1-rasmda o'tkir holati va operatsiyadan keyin. Nodulalar va Absesslarni operativ yorib, drenajlanadi. Antibacterial, yallig’lanishga qarshi va Vitaminoterapiya qilinadi.

2-rasmda bu surunkali past darajada kechgan holati.
Qaysi dorilar "chotki" ta'sir qiladi bu holatda?
πŸ›‘Oral antibiotics
πŸ”° Erythromycin(250-500mg)
πŸ”° Tetracycline(250-500mg)
πŸ”° Clindamycin( 300mg)
πŸ”° Riphampycin(300mg)

πŸ’’ Prednizalon
2-3 kun birinchi 70 mg dozada, keyin 14 kun ichida tushurib boriladi dozasi

Suprastin maz 2 mahal surtishga(yoki boshqa steroid mazlar)

πŸ”†Og'ir holatda
Infliximab tabletkasi(holat bo'yicha)

〽️ Vitaminoterapiya albatta qilishini kerak


@firstaidstep1
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πŸ“Œ Glycogen metabolism by hormones and enzymes

#biochemistry

πŸ”˜ Metabolism in the liver
πŸ”˜ Metabolism in the muscle





πŸ›‘ YouTube πŸ‘‡
https://youtu.be/vqThtIuzMVI?si=ZXjFhtartOcIv1Nc

@firstaidstep1
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πŸ“Œ Glycogen storage disease Part 1

#biochemistry

πŸ”˜ Periodic acid Schiff stain
πŸ”˜ Von Gierke disease(type 1)

πŸ”° Lactic acidosis
πŸ”° Hyperlipidemia
πŸ”° Hepatomegaly
πŸ”° Renomegaly



πŸ›‘ YouTube πŸ‘‡
https://youtu.be/u35_kVELqf0?si=2COW7SZiZopU6mJw



@firstaidstep1
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πŸ“ŒGlycogen storage diseases Part 2
#biochemistry

πŸ”° Cori
πŸ”° Anderson
πŸ”° Pompe
πŸ”° McArdle


πŸ”˜ Cardiomyopathy
πŸ”˜ Hypotonia
πŸ”˜ Exercise intolerance
πŸ”˜ Enlarged tongue
πŸ”˜Myoglobinuria(red urine)
πŸ”˜ Second wind phenomenon

#jonsharipov

πŸ›‘YouTube πŸ‘‡
https://youtu.be/vHOmQeJw8RU?si=Uant_Knvra3RQ6Pj
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πŸ“Œ Lysosomal storage diseases

#biochemistry

πŸ”° Tay-Sachs
πŸ”° Fabry
πŸ”° Metachromatic leukodysrophy
πŸ”° Krabbe disease
πŸ”° Niemann Pick
πŸ”° Gaucher

πŸ”˜ Progressive neurodegeration
πŸ”˜ Developmental delay
πŸ”˜ Hiperreflexia or hiporeflexia
πŸ”˜ Cherry red spot on macula
πŸ”˜ Onion skin
πŸ”˜ Angiokeratomas
πŸ”˜ Hypohidrosis
πŸ”˜ Dementia
πŸ”˜ CN II atrophy
πŸ”˜ Hepatosplenomegaly
πŸ”˜ Osteoporosis
πŸ”˜ Bone crises
πŸ”˜ Necrosis
πŸ”˜ Other tissue cells damage


πŸ›‘ YouTube πŸ‘‡
https://youtu.be/9v7bvGa5WB4?si=l6qNeo7RtWQlPB3S


@firstaidstep1
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πŸ“ŒFatty acid metabolism | Yog' kislota metabolizmi

Synthesis and Degradation

πŸ”° Citrate shuttle
πŸ”° Carnitine shuttle


πŸ”˜ Systemic 1Β° carnitine deficiency
πŸ”˜ Medium-chain Acyl-CoA dehydrogenase deficiency


πŸ—£Steptaker: #jonsharipov

πŸ›‘YouTube πŸ‘‡
https://www.youtube.com/embed/WIlFGpLTRjo
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πŸ“Œ Ketone bodies | Keton tanachalari
#biochemistry

〽️ Aceton
〽️ Acetoacetat
〽️ Ι“-hydroxybutyrate


πŸ”˜ Prolonged starvation
πŸ”˜ Diabetic ketoacidosis
πŸ”˜ Chronic alcohol ovurse
πŸ”˜ Fruty odor


πŸ—£ #jon_sharipov

πŸ›‘ YouTube πŸ‘‡
https://youtu.be/Rt0I_JYgS7s?si=dBM0Uov9MlsegEWE
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